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CASE REPORT
Year : 2015  |  Volume : 59  |  Issue : 1  |  Page : 43-46

Anaesthetic management of a child with panthothenate kinase-associated neurodegeneration


Department of Anaesthesiology, All India Institute of Medical Sciences, New Delhi, India

Correspondence Address:
Dr. Sulagna Bhattacharjee
Department of Anaesthesiology, All India Institute of Medical Sciences, Ansari Nagar, New Delhi - 110 029
India
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Source of Support: None, Conflict of Interest: None


DOI: 10.4103/0019-5049.149449

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Panthothenate kinase-associated neurodegeneration (PKAN) (Hallervorden-Spatz disease) is a rare autosomal recessive chromosomal disorder characterised by progressive neuroaxonal dystrophy. The characteristic features include involuntary movements, rigidity, mental retardation, seizures, emaciation. The anaesthetic concerns include difficult airway, aspiration pneumonia, dehydration, and post-operative respiratory, and renal insufficiency. We report successful anaesthetic management of a 9-year-old intellectually disabled male child with PKAN, scheduled for ophthalmic surgery under general anaesthesia.


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