Indian Journal of Anaesthesia

CASE REPORT
Year
: 2011  |  Volume : 55  |  Issue : 2  |  Page : 187--189

Anaesthetic management of a patient with Eisenmenger syndrome and β-thalassemia major for splenectomy


Nishkarsh Gupta, Sarbjot Kaur, Ajay Goila, Mridula Pawar 
 Department of Anesthesiology and Intensive Care, PGIMER and Associated Dr. RML Hospital, New Delhi, India

Correspondence Address:
Sarbjot Kaur
Department of Anesthesiology and Intensive Care, Room No. 127, Doctors Hostel, Dr. Ram Manohar Lohia Hospital, New Delhi - 01
India

We describe for the first time, the perioperative care of a patient with a rare combination of Eisenmenger syndrome with β-thalassemia major presenting for splenectomy. Patients with Eisenmenger syndrome have polycythemia because of chronic hypoxia but our patient was anaemic and had thrombocytopenia because of thalassemia major. The management of such a case can be challenging for any anaesthesiologist because of severe V/Q mismatch (high shunt fraction and restrictive lung disease because of hypersplenism), decreased oxygen carrying capacity (anaemia) and increased risk of haemorrhage (thrombocytopenia), along with the potential increase in intracardiac shunt during anaesthesia.


How to cite this article:
Gupta N, Kaur S, Goila A, Pawar M. Anaesthetic management of a patient with Eisenmenger syndrome and β-thalassemia major for splenectomy.Indian J Anaesth 2011;55:187-189


How to cite this URL:
Gupta N, Kaur S, Goila A, Pawar M. Anaesthetic management of a patient with Eisenmenger syndrome and β-thalassemia major for splenectomy. Indian J Anaesth [serial online] 2011 [cited 2019 Sep 21 ];55:187-189
Available from: http://www.ijaweb.org/article.asp?issn=0019-5049;year=2011;volume=55;issue=2;spage=187;epage=189;aulast=Gupta;type=0