Indian Journal of Anaesthesia

CASE REPORT
Year
: 2012  |  Volume : 56  |  Issue : 4  |  Page : 394--396

Anaesthetic management in Gorlin-Goltz syndrome


Kundan S Gosavi, Surbhi D Mundada 
 Department of Anaesthesia and Critical Care, Grant Medical College and Sir. J. J. Groups of Hospitals, Mumbai, Maharashtra, India

Correspondence Address:
Surbhi D Mundada
Department of Anaesthesia and Critical Care, Sir. J. J. Group of Hospitals, 51 Rohini Bldg, NOFRA, Colaba (Navy Nagar), Mumbai 400 005, Maharashtra
India

Gorlin-Goltz syndrome is a rare autosomal-dominant syndrome related to mutation in DQ PatchedDQ tumour suppressor gene on chromosome 9. Basocellular carcinomas, odontogenic keratocysts, palmar and/or plantar pits and ectopic calcifications of the falx cerebri are its major features, along with more than 100 minor features. Odontogenic cysts, notorious for recurrence, can make endotracheal intubation difficult, requiring modification of the standard intubation technique. We report such a case managed successfully by awake fibreoptic intubation. Direct laryngoscopy under anaesthesia later confirmed that it was a good decision.


How to cite this article:
Gosavi KS, Mundada SD. Anaesthetic management in Gorlin-Goltz syndrome.Indian J Anaesth 2012;56:394-396


How to cite this URL:
Gosavi KS, Mundada SD. Anaesthetic management in Gorlin-Goltz syndrome. Indian J Anaesth [serial online] 2012 [cited 2020 May 25 ];56:394-396
Available from: http://www.ijaweb.org/article.asp?issn=0019-5049;year=2012;volume=56;issue=4;spage=394;epage=396;aulast=Gosavi;type=0